Hiroshi Manya

Molecular cloning and characterization of rat Pomt1 and Pomt2 (2006)

Manya, Hiroshi, Chiba, Atsuro, Margolis, Richard U., Endo, Tamao

Mammalian O-mannosylation, although an uncommon type of protein modification, is essential for normal brain and muscle development. Defective O-mannosylation causes congenital muscular dystrophy with...

Molecular cloning and characterization of rat Pomt1 and Pomt2 (2006)

Manya, Hiroshi, Chiba, Atsuro, Margolis, Richard U., Endo, Tamao

Mammalian O-mannosylation, although an uncommon type of protein modification, is essential for normal brain and muscle development. Defective O-mannosylation causes congenital muscular dystrophy with...

Molecular cloning and characterization of rat Pomt1 and Pomt2 (2006)

Manya, Hiroshi, Chiba, Atsuro, Margolis, Richard U., Endo, Tamao

Mammalian O-mannosylation, although an uncommon type of protein modification, is essential for normal brain and muscle development. Defective O-mannosylation causes congenital muscular dystrophy with...

Galectin-1 induces astrocyte differentiation, which leads to production of brain-derived neurotrophic factor (2004)

Sasaki, Tasuku, Hirabayashi, Jun, Manya, Hiroshi, Kasai, Ken-ichi, Endo, Tamao

Brain-derived neurotrophic factor (BDNF) is a neuroprotective polypeptide that is thought to be responsible for neuron proliferation, differentiation, and survival. An agent that enhances production...

Worldwide distribution and broader clinical spectrum of muscle-eye-brain disease (2003)

Taniguchi, Kiyomi, Kobayashi, Kazuhiro, Saito, Kayoko, Yamanouchi, Hideo, Ohnuma, Akira, Hayashi, Yukiko K., ...

Muscle–eye–brain disease (MEB), an autosomal recessive disorder prevalent in Finland, is characterized by congenital muscular dystrophy, brain malformation and ocular abnormalities. Since the MEB...

Galectin-1 induces astrocyte differentiation, which leads to production of brain-derived neurotrophic factor (2003)

Sasaki, Tasuku, Hirabayashi, Jun, Manya, Hiroshi, Kasai, Ken-ichi, Endo, Tamao

Brain-derived neurotrophic factor (BDNF) is a neuroprotective polypeptide that is thought to be responsible for neuron proliferation, differentiation and survival. An agent that enhances production...

Galectin-1 induces astrocyte differentiation, which leads to production of brain-derived neurotrophic factor (2003)

Sasaki, Tasuku, Hirabayashi, Jun, Manya, Hiroshi, Kasai, Ken-ichi, Endo, Tamao

Brain-derived neurotrophic factor (BDNF) is a neuroprotective polypeptide that is thought to be responsible for neuron proliferation, differentiation and survival. An agent that enhances production...

A new {{beta}}-1,2-N-acetylglucosaminyltransferase that may play a role in the biosynthesis of mammalian O-mannosyl glycans (2001)

Takahashi, Seiichiro, Sasaki, Tasuku, Manya, Hiroshi, Chiba, Yasunori, Yoshida, Aruto, Mizuno, Mamoru, ...

Recent studies have shown that O-mannosyl glycans are present in several mammalian glycoproteins. Although knowledge on the functional roles of these glycans is accumulating, their biosynthetic...

Comparative Study of the Asparagine-Linked Sugar Chains of Human Lipocalin-Type Prostaglandin D Synthase Purified from Urine and Amniotic Fluid, and Recombinantly Expressed in Chinese Hamster Ovary Cells (2000)

Manya, Hiroshi, Sato, Yuji, Eguchi, Naomi, Seiki, Kousuke, Oda, Hiroshi, Nakajima, Hiroshi, ...

Lipocalin-type prostaglandin D synthase (L-PGDS) is a highly glycosylated member of the lipocalin gene family and is secreted into various human body fluids. We comparatively analyzed the structures...

Demonstration of mammalian protein O-mannosyltransferase activity: Coexpression of POMT1 and POMT2 required for enzymatic activity

Manya, Hiroshi, Chiba, Atsuro, Yoshida, Aruto, Wang, Xiaohui, Chiba, Yasunori, Jigami, Yoshifumi, ...

Defects in O-mannosylation of α-dystroglycan are thought to cause certain types of congenital muscular dystrophies with neuronal migration disorders. Among these muscular dystrophies,...

Demonstration of mammalian protein O-mannosyltransferase activity: Coexpression of POMT1 and POMT2 required for enzymatic activity

Manya, Hiroshi, Chiba, Atsuro, Yoshida, Aruto, Wang, Xiaohui, Chiba, Yasunori, Jigami, Yoshifumi, ...

Defects in O-mannosylation of α-dystroglycan are thought to cause certain types of congenital muscular dystrophies with neuronal migration disorders. Among these muscular dystrophies,...