R. M. Freedom

Results of right atrial to right ventricular and right atrial to pulmonary artery conduits for complex congenital heart disease.

Laks, H, Williams, W G, Hellenbrand, W E, Freedom, R M, Talner, N S, Rowe, R D, ...

The Fontan procedure was initially proposed for tricuspid atresia (TA). We describe our experience with modifications of this operation and its application to previously uncorrectable congenital...

Results with the Mustard operation in simple transposition of the great arteries 1963-1985.

Trusler, G A, Williams, W G, Duncan, K F, Hesslein, P S, Benson, L N, Freedom, R M, ...

From May 1963 to December 1985, 329 infants and children underwent repair of simple transposition of the great arteries (TGA) using Mustard's technique. To assess improvement, the patients were...

Results of right atrial to right ventricular and right atrial to pulmonary artery conduits for complex congenital heart disease.

Laks, H, Williams, W G, Hellenbrand, W E, Freedom, R M, Talner, N S, Rowe, R D, ...

The Fontan procedure was initially proposed for tricuspid atresia (TA). We describe our experience with modifications of this operation and its application to previously uncorrectable congenital...

Results with the Mustard operation in simple transposition of the great arteries 1963-1985.

Trusler, G A, Williams, W G, Duncan, K F, Hesslein, P S, Benson, L N, Freedom, R M, ...

From May 1963 to December 1985, 329 infants and children underwent repair of simple transposition of the great arteries (TGA) using Mustard's technique. To assess improvement, the patients were...

The prostaglandin challenge. Test to unmask obstructed total anomalous pulmonary venous connections in asplenia syndrome.

Freedom, R M, Olley, P M, Coceani, F, Rowe, R D

The patient with complex congenital heart disease, severe pulmonary outflow obstruction, and visceral heterotaxia, may have 'silent' obstruction of the pulmonary venous return. Severe reduction of...

Rapid evolution from "normal" left ventricular outflow tract to fatal subaortic stenosis in infancy.

Freedom, R M, Fowler, R S, Duncan, W J

Serial clinical, echocardiographic, haemodynamic, and angiocardiographic data support the conclusion that over four months severe discrete subaortic stenosis evolved from a previously...

Torsade de pointes ventricular tachycardia in a newborn infant.

Finley, J P, Radford, D J, Freedom, R M

A case of paroxysmal ventricular tachycardia of torsade de pointes variety occurring in a newborn infant is described. A rare problem in the newborn, ventricular tachycardia has been associated with...

Anatomical variants in aortic atresia. Potential candidates for ventriculoaortic reconstitution.

Freedom, R M, Williams, W G, Dische, M R, Rowe, R D

Aortic valve atresia is usually associated with severe hypoplasia of the left ventricle and mitral apparatus. Palliative procedures, including atrial septectomy, pulmonary artery-aorta anastomosis,...

Right to left interatrial communications after the modified Fontan procedure: identification and management with transcatheter occlusion.

Hsu, H. S., Nykanen, D. G., Williams, W. G., Freedom, R. M., Benson, L. N.

OBJECTIVE--To describe unusual venous communications from the right to the left atrium resulting in cyanosis after the modified Fontan procedure, and their management with transcatheter occlusion....

Endovascular stents in children under 1 year of age: acute impact and late results.

Hatai, Y., Nykanen, D. G., Williams, W. G., Freedom, R. M., Benson, L. N.

OBJECTIVES--To review efficacy and safety of endovascular stent implants in children < 1 year of age with congenital heart lesions. DESIGN--Retrospective study of patients in a tertiary care setting....

Profile of paediatric patients with pulmonary hypertension judged by responsiveness to vasodilators.

Houde, C, Bohn, D J, Freedom, R M, Rabinovitch, M

OBJECTIVE--To describe the demographic and haemodynamic variables of children presenting with primary pulmonary hypertension or pulmonary hypertension appearing or persisting after surgical...

The morphology of the right ventricular outflow tract after percutaneous pulmonary valvotomy: long term follow up.

Robertson, M, Benson, L N, Smallhorn, J S, Musewe, N, Freedom, R M, Moes, C A, ...

Twenty nine patients (19 male, mean (SD) age 6.25 (0.5) years (range 0.16-15 years] with typical pulmonary valve stenosis were treated by balloon dilatation of the pulmonary valve. They were studied...

Abnormal cardiac signs after Fontan type of operation: indicators of residua and sequelae.

Leung, M P, Benson, L N, Smallhorn, J F, Williams, W G, Trusler, G A, Freedom, R M

Among 74 survivors of the Fontan type of operation abnormal cardiac signs were detected in 46 (62%) at postoperative examination. The findings were analysed in relation to the state of the...

Determination of left ventricular volumes by Simpson's rule in infants and children with congenital heart disease.

Ino, T, Benson, L N, Mikalian, H, Freedom, R M, Rowe, R D

Regression equations were developed from left ventricular casts of known volumes to calculate left ventricular volumes from biplane cineangiography obtained in non-standard views. Volumes were...

Distinguishing between anomalous origin of the left coronary artery from the pulmonary trunk and dilated cardiomyopathy: role of echocardiographic measurement of the right coronary artery diameter.

Koike, K, Musewe, N N, Smallhorn, J F, Freedom, R M

Patients with anomalous origin of the left coronary artery from the pulmonary trunk usually have a large right coronary artery. This study examines the diagnostic value of measuring the diameter of...

Balloon dilatation of congenital aortic valve stenosis in infants and children: short term and intermediate results.

Vogel, M, Benson, L N, Burrows, P, Smallhorn, J F, Freedom, R M

Percutaneous balloon dilatation of the aortic valve was attempted in 25 consecutive patients with stenosis. The aortic valve diameters were normal for age. The balloon catheters were placed...

The dysplastic pulmonary valve: echocardiographic features and results of balloon dilatation.

Musewe, N N, Robertson, M A, Benson, L N, Smallhorn, J F, Burrows, P E, Freedom, R M, ...

The feasibility of using balloon dilatation to relieve stenosis caused by dysplasia of the pulmonary valve was assessed in seven patients (five female, mean age two years) with angiographically...

Familial desminopathy: myopathy with accumulation of desmin-type intermediate filaments.

Vajsar, J, Becker, L E, Freedom, R M, Murphy, E G

Two siblings developed cardiomyopathy several years before slowly progressive muscle weakness. Skeletal muscle biopsy specimens showed subsarcolemmal crescents of dark eosinophilic material in both...