Yoshihiro Fujimura

Successful Treatment of Primitive Neuroectodermal Tumor-associated Microangiopathy with Multiple Bone Metastases (2007)

Morishita, Toru, Matsumoto, Masanori, Honoki, Kanya, Yoshida, Atsushi, Takakura, Yoshinori, Fujimura, Yoshihiro

We report here a 16-year-old male with primitive neuroectodermal tumor (PNET)-associated probable microangiopathy with multiple bone metastases. Laboratory findings excluded the possibility of...

Novel compound heterozygote mutations (H234Q/R1206X) of the ADAMTS13 gene in an adult patient with Upshaw-Schulman syndrome showing predominant episodes of repeated acute renal failure (2006)

Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...

Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw-Schulman syndrome (USS)...

Novel compound heterozygote mutations (H234Q/R1206X) of the ADAMTS13 gene in an adult patient with Upshaw-Schulman syndrome showing predominant episodes of repeated acute renal failure (2006)

Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...

Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw–Schulman syndrome...

Novel compound heterozygote mutations (H234Q/R1206X) of the ADAMTS13 gene in an adult patient with Upshaw-Schulman syndrome showing predominant episodes of repeated acute renal failure (2006)

Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...

Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw–Schulman syndrome...

Novel compound heterozygote mutations (H234Q/R1206X) of the ADAMTS13 gene in an adult patient with Upshaw-Schulman syndrome showing predominant episodes of repeated acute renal failure (2006)

Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...

Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw-Schulman syndrome (USS)...

Interaction of von Willebrand Factor with the Extracellular Matrix and Glycocalicin under Static Conditions (1997)

Matsui, Taei, Kunishima, Shinji, Hamako, Jiharu, Katayama, Masahiko, Kamiya, Tadashi, Naoe, Tomoki, ...

The binding of human von Willebrand factor (vWF) to a variety of extracellular matrix components immobilized on plates and the binding of vWF to platelet glycoprotein Ib (GPIb) after interacting with...

Fibronectin and 130-kDa Molecule Complex Mimics Snake Venom Botrocetin-Like Structure Potentially Modulating Association between von Willebrand Factor and Vascular Vessel Wall (1995)

Katayama, Masahiko, Nagata, Satomi, Hirai, Sayuri, Miura, Shuji, Fujimura, Yoshihiro, Matusi, Taei, ...

We established seven hybridomas secreting monoclonal antibodies (MoAbs) against the venom from Bothrops jararaca. Six of them were demonstrated to specifically recognize botrocetin, a venom protein...

Blood Clotting Factor IX Kashihara: Amino Acid Substitution of Valine-182 by Phenylalanine (1989)

Sakai, Toshiyuki, Yoshioka, Akira, Yamamoto, Kazukuni, Niinomi, Koh, Fujimura, Yoshihiro, Fukui, Hiromu, ...

Hemophilia B Kashihara is a severe hemorrhagic disorder in which the factor IX antigen is present in normal amounts but factor IX biological activity is markedly reduced. In addition, purified factor...

Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor-cleaving protease activity

Kokame, Koichi, Matsumoto, Masanori, Soejima, Kenji, Yagi, Hideo, Ishizashi, Hiromichi, Funato, Masahisa, ...

von Willebrand factor (VWF) is synthesized primarily in vascular endothelial cells and secreted into the plasma as unusually large VWF multimers. Normally, these multimers are quickly degraded into...

Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor-cleaving protease activity

Kokame, Koichi, Matsumoto, Masanori, Soejima, Kenji, Yagi, Hideo, Ishizashi, Hiromichi, Funato, Masahisa, ...

von Willebrand factor (VWF) is synthesized primarily in vascular endothelial cells and secreted into the plasma as unusually large VWF multimers. Normally, these multimers are quickly degraded into...