Takemoto, Yasuhiro, Kawata, Hiroyuki, Imagawa, Keiichi, Soeda, Tsunenari, Somekawa, Satoshi, Uemura, Shiro, ...
Morishita, Toru, Matsumoto, Masanori, Honoki, Kanya, Yoshida, Atsushi, Takakura, Yoshinori, Fujimura, Yoshihiro
We report here a 16-year-old male with primitive neuroectodermal tumor (PNET)-associated probable microangiopathy with multiple bone metastases. Laboratory findings excluded the possibility of...
Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...
Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw-Schulman syndrome (USS)...
Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...
Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw–Schulman syndrome...
Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...
Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw–Schulman syndrome...
Shibagaki, Yugo, Matsumoto, Masanori, Kokame, Koichi, Ohba, Shigeyoshi, Miyata, Toshiyuki, Fujimura, Yoshihiro, ...
Background. Unlike acquired thrombotic thrombocytopenic purpura or haemolytic uraemic syndrome, which are often intractable, thrombotic microangiopathy in patients with Upshaw-Schulman syndrome (USS)...
Matsui, Taei, Kunishima, Shinji, Hamako, Jiharu, Katayama, Masahiko, Kamiya, Tadashi, Naoe, Tomoki, ...
The binding of human von Willebrand factor (vWF) to a variety of extracellular matrix components immobilized on plates and the binding of vWF to platelet glycoprotein Ib (GPIb) after interacting with...
Katayama, Masahiko, Nagata, Satomi, Hirai, Sayuri, Miura, Shuji, Fujimura, Yoshihiro, Matusi, Taei, ...
We established seven hybridomas secreting monoclonal antibodies (MoAbs) against the venom from Bothrops jararaca. Six of them were demonstrated to specifically recognize botrocetin, a venom protein...
Blood Clotting Factor IX Kashihara: Amino Acid Substitution of Valine-182 by Phenylalanine (1989)
Sakai, Toshiyuki, Yoshioka, Akira, Yamamoto, Kazukuni, Niinomi, Koh, Fujimura, Yoshihiro, Fukui, Hiromu, ...
Hemophilia B Kashihara is a severe hemorrhagic disorder in which the factor IX antigen is present in normal amounts but factor IX biological activity is markedly reduced. In addition, purified factor...
Kokame, Koichi, Matsumoto, Masanori, Soejima, Kenji, Yagi, Hideo, Ishizashi, Hiromichi, Funato, Masahisa, ...
von Willebrand factor (VWF) is synthesized primarily in vascular endothelial cells and secreted into the plasma as unusually large VWF multimers. Normally, these multimers are quickly degraded into...
Kokame, Koichi, Matsumoto, Masanori, Soejima, Kenji, Yagi, Hideo, Ishizashi, Hiromichi, Funato, Masahisa, ...
von Willebrand factor (VWF) is synthesized primarily in vascular endothelial cells and secreted into the plasma as unusually large VWF multimers. Normally, these multimers are quickly degraded into...